Article No
GTX01987
Galactosidase alpha
Galactosidase alpha antibody [001]
Antibodies Primary
Specifications
| Application | IP, WB |
| Article No | GTX01987 |
| Country Availability | SE, FI, DK, NO, IS, EE, LV, LT |
| Clone | 1 |
| Clone Type | monoclonal |
| Conjugation | Unconjugated |
| Description | Galactosidase alpha antibody [001] |
| Supplier | GeneTex |
| Entrez Gene ID | 2717 |
| Gene Symbol | GLA |
| Immunogen | Recombinant Human alpha-Galactosidase A / GLA protein |
| Isotype | IgG |
| Notes | This gene encodes a homodimeric glycoprotein that hydrolyses the terminal alpha-galactosyl moieties from glycolipids and glycoproteins. This enzyme predominantly hydrolyzes ceramide trihexoside, and it can catalyze the hydrolysis of melibiose into galactose and glucose. A variety of mutations in this gene affect the synthesis, processing, and stability of this enzyme, which causes Fabry disease, a rare lysosomal storage disorder that results from a failure to catabolize alpha-D-galactosyl glycolipid moieties. [provided by RefSeq, Jul 2008] |
| Product Type | Antibodies Primary |
| Protocol | WB: 1:1000-1:5000. IP: 4-6 µl/mg of lysate. *Optimal dilutions/concentrations should be determined by the researcher.Not tested in other applications. |
| Purification | Protein A Purified |
| Size | 100µl |
| Source / Host | rabbit |
| Species Reactivity | human |
| Storage | 4°C, -80°C |
| UniProt Number | P06280 |
| Product Page Updated | 2024-01-03T10:31:47.950Z |
